We discuss the following disorders of adaptive immune system resulting in primary immunodeficiency:
B-cell disorders: Agammaglobulinemia (including Bruton's), Selective IG deficiency (including selective IgA deficiency), Common Variable Immunodeficiency
T-cell Disorders: DiGeroge, IL-12 receptor pathway disorders (Mendelian Susceptibility to Mycobacterial Infection), Chronic Mucocutaneous Candidiasis
Combined B & T cell disorders: Severe combined immunodeficiency (SCID), Autosomal- Dominant Hyper-IgE Syndrome, Wiskott-Aldrich, Ataxia-Telangiectasia, Hyper-IgM syndrome